ACUTE-PANCREATITIS IN PROPIONIC ACIDEMIA

被引：22

作者：

BURLINA, AB ^{[1
]}

DIONISIVICI, C ^{[1
]}

PIOVAN, S ^{[1
]}

SAPONARA, I ^{[1
]}

BARTULI, A ^{[1
]}

SABETTA, G ^{[1
]}

ZACCHELLO, F ^{[1
]}

机构：

[1] OSPED BAMBINO GESU,ROME,ITALY

来源：

JOURNAL OF INHERITED METABOLIC DISEASE | 1995年 / 18卷 / 02期

关键词：

D O I：

10.1007/BF00711758

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

It is well known that patients with organic acidurias, aminoacidopathies and congenital hyperammonaemias often show gastrointestinal dysfunction including feeding refusal, nausea, vomiting and gastro-oesophageal and abdominal pain during episodes of acute metabolic decompensation. In some cases, signs of gastrointestinal dysfunction may also be present when they are metabolically stable. More recently, acute pancreatitis, a rather uncommon condition in childhood, has been reported in patients with disorders of branched-chain organic acid metabolism (Kahler et al 1994). We describe two unrelated children with propionic acidaemia complicated by acute pancreatitis. To our knowledge, this is the first report of acute pancreatitis in propionic acidaemia.

引用

页码：169 / 172

页数：4

共 10 条

[1] INTERACTION BETWEEN VALPROATE AND BRANCHED-CHAIN AMINO-ACID-METABOLISM [J].