EXTRACORPOREAL ENZYME REACTORS FOR DEPLETION OF PHENYLALANINE IN PHENYLKETONURIA

被引:26
作者
AMBRUS, CM
ANTHONE, S
HORVATH, C
KALGHATGI, K
LELE, AS
EAPEN, G
AMBRUS, JL
RYAN, AJ
LI, P
机构
[1] SUNY BUFFALO, SCH MED, ROSWELL PK MEM INST, DEPT GYNECOL OBSTET, BUFFALO, NY 14214 USA
[2] SUNY BUFFALO, SCH MED, ROSWELL PK MEM INST, DEPT SURG, BUFFALO, NY 14214 USA
[3] SUNY BUFFALO, SCH MED, ROSWELL PK MEM INST, DEPT MED & PEDIAT, BUFFALO, NY 14214 USA
[4] W SENECA DEV CTR, W SENECA, NY USA
[5] YALE UNIV, DEPT CHEM ENGN, NEW HAVEN, CT 06520 USA
关键词
D O I
10.7326/0003-4819-106-4-531
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:531 / 537
页数:7
相关论文
共 45 条
[1]  
AMBRUS CM, 1982, RES COMMUN CHEM PATH, V37, P105
[2]  
AMBRUS CM, 1983, J PHARMACOL EXP THER, V224, P598
[3]   PHENYLALANINE DEPLETION FOR MANAGEMENT OF PHENYLKETONURIA - USE OF ENZYME REACTORS WITH IMMOBILIZED ENZYMES [J].
AMBRUS, CM ;
AMBRUS, JL ;
HORVATH, C ;
PEDERSEN, H ;
SHARMA, S ;
KANT, C ;
MIRAND, E ;
GUTHRIE, R ;
PAUL, T .
SCIENCE, 1978, 201 (4358) :837-839
[4]  
[Anonymous], 1980, BRIT J OBSTET GYNAEC, V87, P839
[5]  
BICKEL H, 1973, BIBL NUTR DIET, V18, P181
[6]  
Blau K., 1979, AROMATIC AMINO ACID, P79
[7]  
BROWN ES, 1971, PEDIATRICS, V48, P401
[8]  
CHANG TMS, 1977, BIOMEDICAL APPLICATI, V2
[9]   SUCCESSFUL PREGNANCY FOLLOWING HEMODIALYSIS AND PYELOPLASTY [J].
DAVID, AS ;
NEWLING, DWW ;
FARR, MJ .
NEPHRON, 1983, 34 (01) :64-66
[10]  
Fiddler M B, 1980, Birth Defects Orig Artic Ser, V16, P143