GENERALIZED N-ACETYLNEURAMINIC ACID STORAGE DISEASE - QUANTITATION AND IDENTIFICATION OF THE MONOSACCHARIDE ACCUMULATING IN BRAIN AND OTHER TISSUES

被引:53
作者
HANCOCK, LW
THALER, MM
HORWITZ, AL
DAWSON, G
机构
[1] UNIV CHICAGO, PRITZKER SCH MED, DEPT PEDIAT, CHICAGO, IL 60637 USA
[2] UNIV CHICAGO, PRITZKER SCH MED, DEPT BIOCHEM, CHICAGO, IL 60637 USA
[3] UNIV CALIF SAN FRANCISCO, MED CTR, DEPT PEDIAT, SAN FRANCISCO, CA 94143 USA
关键词
D O I
10.1111/j.1471-4159.1982.tb08701.x
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:803 / 809
页数:7
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