NORMAL MUSCLE CPT1 AND CPT2 ACTIVITIES IN HEPATIC PRESENTATION PATIENTS WITH CPT1 DEFICIENCY IN FIBROBLASTS - TISSUE SPECIFIC ISOFORMS OF CPT1

被引:42
作者
TEIN, I
DEMAUGRE, F
BONNEFONT, JP
SAUDUBRAY, JM
机构
[1] HOP ENFANTS MALADES,INSERM,U12,UNITE RECH GENET MED,PARIS,FRANCE
[2] CHU NECKER ENFANTS MALAD,DEPT BIOCHIM,F-75730 PARIS 15,FRANCE
关键词
D O I
10.1016/0022-510X(89)90139-1
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:229 / 245
页数:17
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