IRON THERAPY FOR HEPATIC-DYSFUNCTION IN ERYTHROPOIETIC PROTOPORPHYRIA

被引:51
作者
GORDEUK, VR
BRITTENHAM, GM
HAWKINS, CW
MUKHTAR, H
BICKERS, DR
机构
[1] CLEVELAND METROPOLITAN GEN HOSP, DEPT MED, 3395 SCRANTON RD, CLEVELAND, OH 44109 USA
[2] UNIV HOSP CLEVELAND, DEPT DERMATOL, CLEVELAND, OH 44106 USA
[3] CASE WESTERN RESERVE UNIV, WADE PK VET ADM HOSP, CLEVELAND, OH 44106 USA
关键词
D O I
10.7326/0003-4819-105-1-27
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:27 / 31
页数:5
相关论文
共 34 条
[1]   ERYTHROPOIETIC PROTOPORPHYRIA PROVOKED BY IRON THERAPY [J].
BAKER, H .
PROCEEDINGS OF THE ROYAL SOCIETY OF MEDICINE-LONDON, 1971, 64 (06) :610-&
[2]   EFFECTS OF SUCCINYLACETONE ON DIMETHYLSULFOXIDE-MEDIATED INDUCTION OF HEME PATHWAY ENZYMES IN MOUSE FRIEND VIRUS-TRANSFORMED ERYTHROLEUKEMIA-CELLS [J].
BEAUMONT, C ;
DEYBACH, JC ;
GRANDCHAMP, B ;
DASILVA, V ;
DEVERNEUIL, H ;
NORDMANN, Y .
EXPERIMENTAL CELL RESEARCH, 1984, 154 (02) :474-484
[3]   TRANSFUSION THERAPY IN A PATIENT WITH ERYTHROPOIETIC PROTOPORPHYRIA [J].
BECHTEL, MA ;
BERTOLONE, SJ ;
HODGE, SJ .
ARCHIVES OF DERMATOLOGY, 1981, 117 (02) :99-101
[4]   TREATMENT OF THE PORPHYRIAS - MECHANISMS OF ACTION [J].
BICKERS, DR .
JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1981, 77 (01) :107-113
[5]   HEPATIC DISEASE IN ERYTHROPOIETIC PROTOPORPHYRIA [J].
BLOOMER, JR ;
PHILLIPS, MJ ;
DAVIDSON, DL ;
KLATSKIN, G .
AMERICAN JOURNAL OF MEDICINE, 1975, 58 (06) :869-882
[6]   STUDY OF FACTORS CAUSING EXCESS PROTOPORPHYRIN ACCUMULATION IN CULTURED SKIN FIBROBLASTS FROM PATIENTS WITH PROTOPORPHYRIA [J].
BLOOMER, JR ;
BRENNER, DA ;
MAHONEY, MJ .
JOURNAL OF CLINICAL INVESTIGATION, 1977, 60 (06) :1354-1361
[7]  
BLOOMER JR, 1982, GASTROENTEROLOGY, V82, P569
[8]   HEME SYNTHETASE DEFICIENCY IN HUMAN PROTOPORPHYRIA - DEMONSTRATION OF DEFECT IN LIVER AND CULTURED SKIN FIBROBLASTS [J].
BONKOWSKY, HL ;
BLOOMER, JR ;
EBERT, PS ;
MAHONEY, MJ .
JOURNAL OF CLINICAL INVESTIGATION, 1975, 56 (05) :1139-1148
[9]  
Bothwell TH, 1979, IRON METABOLISM MAN
[10]  
BOTTOMLEY SS, 1975, J LAB CLIN MED, V86, P126