THE SUBCELLULAR-LOCALIZATION OF PHYTANIC ACID OXIDASE IN RAT-LIVER

被引:48
作者
SKJELDAL, OH
STOKKE, O
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D O I
10.1016/0005-2760(87)90167-6
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
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页码:38 / 42
页数:5
相关论文
共 20 条
[1]   URINARY-EXCRETION OF DICARBOXYLIC-ACIDS FROM PATIENTS WITH THE ZELLWEGER SYNDROME - IMPORTANCE OF PEROXISOMES IN BETA-OXIDATION OF DICARBOXYLIC-ACIDS [J].
BJORKHEM, I ;
BLOMSTRAND, S ;
HAGA, P ;
KASE, BF ;
PALONEK, E ;
PEDERSEN, JI ;
STRANDVIK, B ;
WIKSTROM, SA .
BIOCHIMICA ET BIOPHYSICA ACTA, 1984, 795 (01) :15-19
[2]   SUCCINIC DEHYDROGENASE [J].
BONNER, WD .
METHODS IN ENZYMOLOGY, 1955, 1 :722-729
[3]  
BROWN FR, 1982, JOHNS HOPKINS MED J, V151, P344
[4]   ASSAY OF CATALASES AND PEROXIDASES [J].
CHANCE, B ;
MAEHLY, AC .
METHODS IN ENZYMOLOGY, 1955, 2 :764-775
[5]   DEFICIENCY OF ENZYMES CATALYZING THE BIOSYNTHESIS OF GLYCEROL ETHER LIPIDS IN ZELLWEGER SYNDROME - A NEW CATEGORY OF METABOLIC DISEASE INVOLVING THE ABSENCE OF PEROXISOMES [J].
DATTA, NS ;
WILSON, GN ;
HAJRA, AK .
NEW ENGLAND JOURNAL OF MEDICINE, 1984, 311 (17) :1080-1083
[6]   PEROXISOMAL AND MITOCHONDRIAL DEFECTS IN CEREBRO-HEPATO-RENAL SYNDROME [J].
GOLDFISCHER, S ;
MOORE, CL ;
JOHNSON, AB ;
SPIRO, AJ ;
VALSAMIS, MP ;
WISNIEWSKI, HK ;
RITCH, RH ;
NORTON, WT ;
RAPIN, I ;
GARTNER, LM .
SCIENCE, 1973, 182 (4107) :62-64
[7]   DEFECTS OF BILE-ACID SYNTHESIS IN ZELLWEGER SYNDROME [J].
HANSON, RF ;
SZCZEPANIKVANLEEUWEN, P ;
WILLIAMS, GC ;
GRABOWSKI, G ;
SHARP, HL .
SCIENCE, 1979, 203 (4385) :1107-1108
[8]   SEVERE PLASMALOGEN DEFICIENCY IN TISSUES OF INFANTS WITHOUT PEROXISOMES (ZELLWEGER SYNDROME) [J].
HEYMANS, HSA ;
SCHUTGENS, RBH ;
TAN, R ;
VANDENBOSCH, H ;
BORST, P .
NATURE, 1983, 306 (5938) :69-70
[9]   CONVERSION OF PHYTOL INTO DIHYDROPHYTOL AND PHYTANIC ACID [J].
JELLUM, E ;
ELDJARN, L ;
TRY, K .
ACTA CHEMICA SCANDINAVICA, 1966, 20 (09) :2535-&
[10]   NEONATAL ADRENOLEUKODYSTROPHY - NEW CASES, BIOCHEMICAL-STUDIES, AND DIFFERENTIATION FROM ZELLWEGER AND RELATED PEROXISOMAL POLYDYSTROPHY SYNDROMES [J].
KELLEY, RI ;
DATTA, NS ;
DOBYNS, WB ;
HAJRA, AK ;
MOSER, AB ;
NOETZEL, MJ ;
ZACKAI, EH ;
MOSER, HW .
AMERICAN JOURNAL OF MEDICAL GENETICS, 1986, 23 (04) :869-901