FAMILIAL RELATIVE POLYCYTHEMIA DUE TO HEMOGLOBIN HEATHROW

被引:2
作者
BEARD, MEJ
HAMER, JW
BRENNAN, SO
JONES, JN
SHEAT, JM
MACLAURIN, JS
机构
[1] CHRISTCHURCH HOSP,DEPT BIOCHEM,CHRISTCHURCH,NEW ZEALAND
[2] PRINCESS MARGARET HOSP,DEPT RESP MED,CHRISTCHURCH,NEW ZEALAND
来源
AUSTRALIAN AND NEW ZEALAND JOURNAL OF MEDICINE | 1979年 / 9卷 / 03期
关键词
D O I
10.1111/j.1445-5994.1979.tb04143.x
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Summary: Eleven affected members of a New Zealand family carrying the high oxygen affinity haemoglobin Heathrow are described. The detection of high oxygen affinity abnormal haemoglobins may be difficult as haemoglobin and red cell mass may both fall within the normal range and no abnormality may be detected on haemoglobin electrophoresis or by haemoglobin stability tests. The importance of oxygen affinity studies to establish the diagnosis is emphasized. Copyright © 1979, Wiley Blackwell. All rights reserved
引用
收藏
页码:297 / 301
页数:5
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