CONGENITAL JUVENILE GRANULOSA-CELL TUMOR OF THE TESTIS - REPORT OF A CASE SHOWING EXTENSIVE DEGENERATIVE CHANGES

被引:23
作者
CHAN, JKC [1 ]
CHAN, VSM [1 ]
MAK, KL [1 ]
机构
[1] QUEEN ELIZABETH HOSP,PAEDIAT UNIT A,KOWLOON,HONG KONG
关键词
juvenile granulosa cell tumour; testicular cysts; testicular tumour;
D O I
10.1111/j.1365-2559.1990.tb00666.x
中图分类号
Q2 [细胞生物学];
学科分类号
071009 ; 090102 ;
摘要
Juvenile granulosa cell tumour is a rare neoplasm of the testis which occurs predominantly in infancy and which may be associated with sex chromosomal abnormalities. We report an unusual case with deceptive histological features resulting from extensive degenerative changes. In the particulated intra‐abdominal mass resected from a 1‐month‐old male baby with 45,X/46,X,iso(Yq) mosaicism, there were multiple large cystic spaces devoid of cellular lining or lined by flat nondescript cells, mimicking various cystic lesions such as multicystic mesothelioma, cystic lymphangioma and cystic dysplasia. The cysts were separated by a highly vascularized fibrous stroma. Only in very rare cysts and the smaller cysts in the region of the pedicle were granulosa cells identified, permitting a diagnosis of juvenile granulosa cell tumour to be made. Copyright © 1990, Wiley Blackwell. All rights reserved
引用
收藏
页码:75 / 80
页数:6
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