SOMATOSTATINOMA OF THE PANCREAS ASSOCIATED WITH VON HIPPEL-LINDAU DISEASE

被引：17

作者：

MAKI, M ^{[1
]}

KANEKO, Y ^{[1
]}

OHTA, Y ^{[1
]}

NAKAMURA, T ^{[1
]}

MACHINAMI, R ^{[1
]}

KUROKAWA, K ^{[1
]}

机构：

[1] UNIV TOKYO,FAC MED,DEPT PATHOL,BUNKYO KU,TOKYO 113,JAPAN

来源：

INTERNAL MEDICINE | 1995年 / 34卷 / 07期

关键词：

RENAL CELL CARCINOMA; ISLET CELL TUMOR; LIVER METASTASIS; RENAL CYST;

D O I：

10.2169/internalmedicine.34.661

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

A 39-year-old man was admitted because of lumbago, vomiting and massive gastrointestinal bleeding, Oliguria developed a few days later, which was followed by hyperkalemia and cardiac arrest, Autopsy disclosed multiple renal cell carcinomas with diffuse metastasis to the liver, adrenal gland, psoas muscle and vertebrae, In addition, a somatostatinoma was found in the pancreas, From these findings and past history of cerebellar hemangioblastoma and spinal hemangioma he was diagnosed to have von Hippel-Lindau disease, Von Hippel-Lindau disease with islet cell tumor is very rare and is reported here with a review of literature.

引用

页码：661 / 665

页数：5

共 20 条

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