DEMYELINATION AND REMYELINATION AND ONION BULB IN CEREBROTENDINOUS XANTHOMATOSIS

被引：31

作者：

OHNISHI, A

YAMASHITA, Y

GOTO, I

KUROIWA, Y

MURAKAMI, S

IKEDA, M

机构：

[1] KYUSHU UNIV,FAC MED,INST NEUROL,DEPT NEUROL,FUKUOKA,JAPAN

[2] BEPPU NATL HOSP,DEPT NEUROL,BEPPU,JAPAN

[3] KYUSHU UNIV,FAC MED,DEPT PUBL HLTH,FUKUOKA,JAPAN

来源：

ACTA NEUROPATHOLOGICA | 1979年 / 45卷 / 01期

关键词：

Cerebrotendinous xanthomatosis; Onion bubl; Remyelination; Segmental demyelination; Sural nerve;

D O I：

10.1007/BF00691803

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

In a case of cerebrotendinous xanthomatosis (CTX), confirmed biochemically and histologically, quantitative histological studies of the biopsied sural nerve revealed significantly higher incidence of de- and remyelination and onion bulb than in controls. The density of total myelinated fibers fell within the range of controls, although the density of large myelinated fibers seemed to be slightly decreased. It was suggested that the preferential involvement of the myelin sheath and Schwann cell may exist in CTX. © 1979 Springer-Verlag.

引用

页码：43 / 45

页数：3

共 6 条

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DYCK, PJ
STEVENS, JC
MULDER, DW
ESPINOSA, RE
[J]. NEUROLOGY, 1975, 25 (08) : 781 - 785
[3] MURAKAMI S, 1978, CLIN NEUROL, V18, P312
[4] CHOLESTANOLOSIS (CEREBROTENDINOUS XANTHOMATOSIS) - A FOLLOW-UP STUDY ON ORIGINAL FAMILY
PHILIPPART, M
VANBOGAE.L
[J]. ARCHIVES OF NEUROLOGY, 1969, 21 (06) : 603 - +
[5] SCHREINER A, 1975, ACTA NEUROL SCAND, V51, P405
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