WILMS-TUMOR IN THE LI-FRAUMENI CANCER FAMILY SYNDROME

被引:46
作者
HARTLEY, AL
BIRCH, JM
TRICKER, K
WALLACE, SA
KELSEY, AM
HARRIS, M
JONES, PHM
机构
[1] CHRISTIE HOSP NHS TRUST, DEPT PATHOL, MANCHESTER, ENGLAND
[2] DEPT PATHOL, MANCHESTER, ENGLAND
[3] DEPT CHILD HLTH PAEDIAT ONCOL, MANCHESTER, ENGLAND
关键词
D O I
10.1016/0165-4608(93)90166-J
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
Scrutiny of the family pedigrees of a population-based series of 176 children diagnosed with Wilms' tumor between 1954 and 1990, along with a review of the literature on the Li-Fraumeni cancer family syndrome, indicate that Wilms' tumor may be an uncommon component of the syndrome and that a small proportion of children with Wilms' tumor may be members of Li-Fraumeni syndrome (LFS) families.
引用
收藏
页码:133 / 135
页数:3
相关论文
共 21 条
[1]  
BIRCH JM, 1990, CANCER-AM CANCER SOC, V66, P2239, DOI 10.1002/1097-0142(19901115)66:10<2239::AID-CNCR2820661034>3.0.CO
[2]  
2-Q
[3]  
BIRCH JM, 1988, IARC SCI PUBL, V87, P299
[4]   2ND MALIGNANT NEOPLASMS IN SURVIVORS OF WILMS TUMOR - A REPORT FROM THE NATIONAL WILMS TUMOR STUDY [J].
BRESLOW, NE ;
NORKOOL, PA ;
OLSHAN, A ;
EVANS, A ;
DANGIO, GJ .
JNCI-JOURNAL OF THE NATIONAL CANCER INSTITUTE, 1988, 80 (08) :592-595
[5]  
GARBER JE, 1990, CANCER-AM CANCER SOC, V66, P2658, DOI 10.1002/1097-0142(19901215)66:12<2658::AID-CNCR2820661232>3.0.CO
[6]  
2-C
[7]   ADRENAL-CORTICAL TUMORS - EPIDEMIOLOGIC AND FAMILIAL ASPECTS [J].
HARTLEY, AL ;
BIRCH, JM ;
MARSDEN, HB ;
REID, H ;
HARRIS, M ;
BLAIR, V .
ARCHIVES OF DISEASE IN CHILDHOOD, 1987, 62 (07) :683-689
[8]   PATTERNS OF MULTIPLE PRIMARY TUMORS IN PATIENTS TREATED FOR CANCER DURING CHILDHOOD [J].
KINGSTON, JE ;
HAWKINS, MM ;
DRAPER, GJ ;
MARSDEN, HB ;
WILSON, LMK .
BRITISH JOURNAL OF CANCER, 1987, 56 (03) :331-338
[9]  
KOUFOS A, 1989, AM J HUM GENET, V44, P711
[10]  
LAW JC, 1991, CANCER RES, V51, P6385