SCINTIGRAPHIC FINDINGS AND FOLLOW UP IN ERDHEIM-CHESTER DISEASE

被引:46
作者
SANDROCK, D
MERINO, MJ
SCHEFFKNECHT, BHB
NEUMANN, RD
机构
[1] NCI, PATHOL LAB, BETHESDA, MD 20892 USA
[2] NHLBI, CARDIOL BRANCH, BETHESDA, MD 20892 USA
来源
EUROPEAN JOURNAL OF NUCLEAR MEDICINE | 1990年 / 16卷 / 01期
关键词
Bone sclerosis; Erdheim-Chester disease; Lipoidosis;
D O I
10.1007/BF01566013
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
Two cases of Erdheim-Chester disease are presented: a 26-year-old white male patient with lipoidgranulomatosis of numerous long and flat bones and infiltration of pericardium, pleura, liver, spleen, thyroid, skin, conjunctiva, gingiva, and false vocal cord; and a 54-year-old white male with involvement of bones, orbits, brain, pericardium, and retroperitoneum. The scintigraphic findings in this disease are described, and a comprehensive review of the 27 previously reported cases is given including an assessment of the value of scintigraphy for diagnosis and follow up of this rare disease. © 1990 Springer-Verlag.
引用
收藏
页码:55 / 60
页数:6
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