PROGRESSIVE OSSEOUS HETEROPLASIA - A CASE-REPORT

被引:26
作者
ATHANASOU, NA
BENSON, MKD
BRENTON, DP
SMITH, R
机构
[1] NUFFIELD ORTHOPAED CTR,DEPT SURG & MED,OXFORD OX3 7LD,ENGLAND
[2] MIDDLESEX HOSP,ENDOCRINE & METAB UNIT,LONDON,ENGLAND
关键词
ECTOPIC BONE; HETEROPLASIA; ADIPOGENESIS; OSSIFICATION; FIBRODYSPLASIA; OSSIFICANS PROGRESSIVA; MYOSITIS OSSIFICANS;
D O I
10.1016/8756-3282(94)90269-0
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We report the case of a young female who, from infancy, suffered extensive, progressive, heterotopic ossification of her left lower limb. Heterotopic ossification, which was largely but not exclusively intramembranous in type, was most marked in subcutaneous fat but was also noted in muscle and deep connective tissue. The spectrum of changes noted suggests that this congenital disorder of soft tissues is similar to that recently described as progressive osseous heteroplasia.
引用
收藏
页码:471 / 475
页数:5
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