PRIMARY-CARCINOMA OF THE CHOROID-PLEXUS IN LI-FRAUMENI SYNDROME - CASE-REPORT

被引:32
作者
YUASA, H [1 ]
TOKITO, S [1 ]
TOKUNAGA, M [1 ]
机构
[1] KAGOSHIMA MUNICIPAL HOSP, DEPT PATHOL, KAGOSHIMA, JAPAN
关键词
CARCINOMA; CHOROID PLEXUS; LI-FRAUMENI SYNDROME;
D O I
10.1227/00006123-199301000-00021
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
AN 8-MONTH-OLD FEMALE infant with a primary carcinoma of the choroid plexus developed a rhabdomyosarcoma in the anterior chest wall at the age of 1 year and 2 months. Her mother had developed a liposarcoma in her left thigh at the age of 17 years. One of the patient's siblings had a rhabdomyosarcoma of the epipharynx at the age of 1 year. This is the fourth reported case of a choroid plexus carcinoma occurring in Li-Fraumeni syndrome.
引用
收藏
页码:131 / 134
页数:4
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