HB POITIERS [ALPHA-45(CE3)HIS-]ASP] - A NEW HEMOGLOBIN-VARIANT WITH A 2-FOLD INCREASE IN OXYGEN-AFFINITY

被引：15

作者：

BARDAKDJIAN, J

KISTER, J

WAJCMAN, H

BOULARD, P

BOHN, B

BLOUQUIT, Y

GALACTEROS, F

机构：

[1] HOP BICETRE,INSERM,U299,F-94275 LE KREMLIN BICETR,FRANCE

[2] CTR REG TRANSFUS SANGUINE,F-86021 POITIERS,FRANCE

来源：

HEMOGLOBIN | 1994年 / 18卷 / 01期

关键词：

D O I：

10.3109/03630269409014140

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

Hb Poitiers or alpha 45(CE3)His->Asp was found in a 9-year-old French Caucasian boy. The structural modification concerns a heme contact and is responsible for an increased oxygen affinity and a faster than normal rate of autooxidation.

引用

页码：1 / 9

页数：9

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