RECIPROCAL RELATIONSHIP BETWEEN ERYTHROCYTE-ATP AND DEOXY-ATP LEVELS IN INHERITED ADA-DEFICIENCY

被引:26
作者
SIMMONDS, HA
LEVINSKY, RJ
PERRETT, D
WEBSTER, DR
机构
[1] ST BARTHOLOMEWS HOSP,MED UNIT,LONDON EC1A 7BE,ENGLAND
[2] INST CHILD HLTH,DEPT IMMUNOL,LONDON WC1N 1EH,ENGLAND
关键词
D O I
10.1016/0006-2952(82)90325-2
中图分类号
R9 [药学];
学科分类号
1007 ;
摘要
引用
收藏
页码:947 / 951
页数:5
相关论文
共 25 条
[1]  
CARSON DA, 1981, J IMMUNOL, V126, P348
[2]   ADENOSINE-DEAMINASE DEFICIENCY - DISAPPEARANCE OF ADENINE DEOXYNUCLEOTIDES FROM A PATIENTS ERYTHROCYTES AFTER SUCCESSFUL MARROW TRANSPLANTATION [J].
CHEN, SH ;
OCHS, HD ;
SCOTT, CR ;
GIBLETT, ER ;
TINGLE, AJ .
JOURNAL OF CLINICAL INVESTIGATION, 1978, 62 (06) :1386-1389
[3]   ABNORMAL PURINE METABOLISM AND PURINE OVERPRODUCTION IN A PATIENT DEFICIENT IN PURINE NUCLEOSIDE PHOSPHORYLASE [J].
COHEN, A ;
DOYLE, D ;
MARTIN, DW ;
AMMANN, AJ .
NEW ENGLAND JOURNAL OF MEDICINE, 1976, 295 (26) :1449-1454
[4]  
COLEMAN MS, 1978, J BIOL CHEM, V253, P1619
[5]   STUDIES ON ADENINE AND ADENOSINE METABOLISM BY INTACT HUMAN ERYTHROCYTES USING HIGH-PERFORMANCE LIQUID-CHROMATOGRAPHY [J].
DEAN, BM ;
PERRETT, D .
BIOCHIMICA ET BIOPHYSICA ACTA, 1976, 437 (01) :1-15
[6]   CHANGES IN NUCLEOTIDE CONCENTRATIONS IN ERYTHROCYTES OF MAN, RABBIT AND RAT DURING SHORT-TERM STORAGE [J].
DEAN, BM ;
PERRETT, D ;
SENSI, M .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1978, 80 (01) :147-154
[7]   OVERPRODUCTION OF ADENINE DEOXYNUCLEOSIDES AND DEOXYNUCLEOTIDES IN ADENOSINE-DEAMINASE DEFICIENCY WITH SEVERE COMBINED IMMUNODEFICIENCY DISEASE [J].
DONOFRIO, J ;
COLEMAN, MS ;
HUTTON, JJ ;
DAOUD, A ;
LAMPKIN, B ;
DYMINSKI, J .
JOURNAL OF CLINICAL INVESTIGATION, 1978, 62 (04) :884-887
[8]  
HENDERSON JF, 1977, CIBA F S, V48, P3
[9]   INVIVO INACTIVATION OF ERYTHROCYTE S-ADENOSYLHOMOCYSTEINE HYDROLASE BY 2'-DEOXYADENOSINE IN ADENOSINE DEAMINASE-DEFICIENT PATIENTS [J].
HERSHFIELD, MS ;
KREDICH, NM ;
OWNBY, DR ;
OWNBY, H ;
BUCKLEY, R .
JOURNAL OF CLINICAL INVESTIGATION, 1979, 63 (04) :807-811
[10]   PLASMA DEOXYADENOSINE, ADENOSINE, AND ERYTHROCYTE DEOXYATP ARE ELEVATED AT BIRTH IN AN ADENOSINE DEAMINASE-DEFICIENT CHILD [J].
HIRSCHHORN, R ;
ROEGNER, V ;
RUBINSTEIN, A ;
PAPAGEORGIOU, P .
JOURNAL OF CLINICAL INVESTIGATION, 1980, 65 (03) :768-771