DIFFERENTIAL UPTAKE OF HUMAN BETA-GLUCURONIDASE ISOENZYMES FROM SPLEEN BY DEFICIENT FIBROBLASTS

被引：22

作者：

NICOL, DM ^{[1
]}

LAGUNOFF, D ^{[1
]}

PRITZL, P ^{[1
]}

机构：

[1] UNIV WASHINGTON,SCH MED,DEPT PATHOL,SEATTLE,WA 98195

来源：

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS | 1974年 / 59卷 / 03期

关键词：

D O I：

10.1016/S0006-291X(74)80070-7

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：941 / 946

页数：6

共 22 条

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BACH, G ;

WEISSMAN.B ;

FRIEDMAN, R ;

NEUFELD, EF .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1972, 69 (08) :2048-&

[2] IN-VITRO CORRECTION OF DEFICIENT HUMAN FIBROBLASTS BY BETA-GLUCURONIDASE FROM DIFFERENT HUMAN SOURCES [J].

BROT, FE ;

GLASER, JH ;

ROOZEN, KJ ;

SLY, WS .

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1974, 57 (01) :1-8

[3] RABBIT BETA-GLUCURONIDASE - SUBCELLULAR-DISTRIBUTION AND IMMUNOCHEMICAL PROPERTIES [J].

DEAN, RT .

BIOCHEMICAL JOURNAL, 1974, 138 (03) :407-+

[4] BETA-GLUCURONIDASE DEFICIENCY MUCOPOLYSACCHARIDOSIS - STUDIES IN CULTURED FIBROBLASTS [J].

HALL, CW ;

CANTZ, M ;

NEUFELD, EF .

ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1973, 155 (01) :32-38

[5] SIZE AND CHARGE ISOMER SEPARATION AND ESTIMATION OF MOLECULAR WEIGHTS OF PROTENS BY DISC GEL ELECTROPHORESIS [J].

HEDRICK, JL ;

SMITH, AJ .

ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1968, 126 (01) :155-+

[6] RECOGNITION MARKER REQUIRED FOR UPTAKE OF A LYSOSOMAL ENZYME BY CULTURED FIBROBLASTS [J].

HICKMAN, S ;

SHAPIRO, LJ ;

NEUFELD, EF .

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1974, 57 (01) :55-61

[7]

HIGASHINO K, 1971, Medical Journal of Osaka University, V21, P251

[8] ELECTROPHORETIC CHARACTERIZATION OF GLUCOSE DEHYDROGENASE, BETA-GLUCURONIDASE, AND N-ACETYL-BETA-GLUCOSAMINIDASE FROM PLACENTA AND GESTATIONAL SERUM [J].

HUDDLESTON, JF ;

LEE, G ;

ROBINSON, JC .

AMERICAN JOURNAL OF OBSTETRICS AND GYNECOLOGY, 1971, 109 (07) :1017-+

[9]

LAGUNOFF D, 1973, LAB INVEST, V29, P449

[10]

LOWRY OH, 1951, J BIOL CHEM, V193, P265

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