EFFECT OF BETA-ADRENERGIC - BLOCKADE ON AORTIC ROOT RATE OF DILATION IN THE MARFAN-SYNDROME

被引:108
作者
SALIM, MA [1 ]
ALPERT, BS [1 ]
WARD, JC [1 ]
PYERITZ, RE [1 ]
机构
[1] JOHNS HOPKINS MED INST,CTR MED GENET,DEPT MED,BALTIMORE,MD
关键词
D O I
10.1016/0002-9149(94)90762-5
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We recommend that patients with the Marfan syndrome should begin P-adrenergic blocker therapy at the earliest age possible and that the dose be adjusted to the largest dose that is clinically tolerated. Our centers differ with respect to the size of the aorta at the time of recommending onset of therapy. The JHH criteria do not include a size cutoff. The UT experience and recommendation is to treat children with aortic size at or above the 95th percentile. © 1994.
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页码:629 / 633
页数:5
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