TOTAL LIPODYSTROPHY

被引:10
作者
FAIRNEY, A
LEWIS, G
COTTOM, D
机构
[1] Hospital for Sick Children, London W.C.1, Great Ormond Street
[2] St. Mary's Hospital, Portsmouth
关键词
D O I
10.1136/adc.44.235.368
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
A patient with generalized lipodystrophy which was apparent at birth is reported. He showed hepatomegaly, increased growth, and an advanced bone age, together with hirsutism and large external genitalia. Contrary to previous suggestions that the syndrome results from hyperfunction of the anterior pituitary, normal levels for serum insulin and growth hormone were obtained.
引用
收藏
页码:368 / +
页数:1
相关论文
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