CYSTIC-FIBROSIS MICE HAVE ARRIVED

被引:4
作者
HIGGINS, CF [1 ]
TREZISE, AEO [1 ]
机构
[1] UNIV OXFORD, JOHN RADCLIFFE HOSP, IMPERIAL CANC RES LABS, OXFORD OX3 9DU, England
关键词
D O I
10.1093/hmg/1.7.459
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
[No abstract available]
引用
收藏
页码:459 / 460
页数:2
相关论文
共 10 条
[1]   DEMONSTRATION THAT CFTR IS A CHLORIDE CHANNEL BY ALTERATION OF ITS ANION SELECTIVITY [J].
ANDERSON, MP ;
GREGORY, RJ ;
THOMPSON, S ;
SOUZA, DW ;
PAUL, S ;
MULLIGAN, RC ;
SMITH, AE ;
WELSH, MJ .
SCIENCE, 1991, 253 (5016) :202-205
[2]   PURIFICATION AND FUNCTIONAL RECONSTITUTION OF THE CYSTIC-FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR (CFTR) [J].
BEAR, CE ;
LI, CH ;
KARTNER, N ;
BRIDGES, RJ ;
JENSEN, TJ ;
RAMJEESINGH, M ;
RIORDAN, JR .
CELL, 1992, 68 (04) :809-818
[3]  
Boat TF., 1989, CYSTIC FIBROSIS META, V6th, P2649
[4]   DEFECTIVE EPITHELIAL CHLORIDE TRANSPORT IN A GENE-TARGETED MOUSE MODEL OF CYSTIC-FIBROSIS [J].
CLARKE, LL ;
GRUBB, BR ;
GABRIEL, SE ;
SMITHIES, O ;
KOLLER, BH ;
BOUCHER, RC .
SCIENCE, 1992, 257 (5073) :1125-1128
[5]  
COLLEDGE WH, 1992, IN PRESS LANCET
[6]   PROCESSING OF MUTANT CYSTIC-FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR IS TEMPERATURE-SENSITIVE [J].
DENNING, GM ;
ANDERSON, MP ;
AMARA, JF ;
MARSHALL, J ;
SMITH, AE ;
WELSH, MJ .
NATURE, 1992, 358 (6389) :761-764
[7]  
DORIN JR, 1992, IN PRESS NATURE
[8]   HPRT-DEFICIENT (LESCH-NYHAN) MOUSE EMBRYOS DERIVED FROM GERMLINE COLONIZATION BY CULTURED-CELLS [J].
HOOPER, M ;
HARDY, K ;
HANDYSIDE, A ;
HUNTER, S ;
MONK, M .
NATURE, 1987, 326 (6110) :292-295
[9]   A POTENTIAL ANIMAL-MODEL FOR LESCH-NYHAN SYNDROME THROUGH INTRODUCTION OF HPRT MUTATIONS INTO MICE [J].
KUEHN, MR ;
BRADLEY, A ;
ROBERTSON, EJ ;
EVANS, MJ .
NATURE, 1987, 326 (6110) :295-298
[10]   AN ANIMAL-MODEL FOR CYSTIC-FIBROSIS MADE BY GENE TARGETING [J].
SNOUWAERT, JN ;
BRIGMAN, KK ;
LATOUR, AM ;
MALOUF, NN ;
BOUCHER, RC ;
SMITHIES, O ;
KOLLER, BH .
SCIENCE, 1992, 257 (5073) :1083-1088