CARNEY TRIAD - APROPOS OF A NEW CASE

被引:5
作者
ACHA, T [1 ]
PICAZO, B [1 ]
GARCIAMARTIN, FJ [1 ]
URDA, A [1 ]
CAMPOS, J [1 ]
机构
[1] HOSP MATERNO INFANTIL,DEPT PATHOL,MALAGA,SPAIN
来源
MEDICAL AND PEDIATRIC ONCOLOGY | 1994年 / 22卷 / 03期
关键词
CARNEY TRIAD; GASTRIC EPITHELIOID LEIOMYOSARCOMA; PULMONARY CHONDROMA; EXTRAADRENAL PARAGANGLIOMA;
D O I
10.1002/mpo.2950220313
中图分类号
R73 [肿瘤学];
学科分类号
100214 [肿瘤学];
摘要
Carney's triad is defined by the coexistence of at least two of three rare disorders, including gastric epithelioid leiomyosarcoma (malignant leiomyoblastoma), pulmonary chondroma, and paraganglioma, most often extra-adrenal and functioning. We report a new case in a 10-year-old girl. The paraganglioma, although nonfunctioning, was detected after it was searched for, as Carney's triad was suspected. Unrelated seems the development of breast fibroadenomas in the same patient. Whenever a patient with one component of the triad is encountered, the possibility of this syndrome should be considered and the other two components sought. (C) 1994 Wiley-Liss, Inc.
引用
收藏
页码:216 / 220
页数:5
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