POSTOPERATIVE METABOLIC DECOMPENSATION IN MAPLE-SYRUP-URINE-DISEASE IS COMPLETELY PREVENTED BY INSULIN

被引：3

作者：

BIGGEMANN, B

ZASS, R

WENDEL, U

机构：

[1] Universitäts-Kinderklinik, Heinrich-Heine Universität, Düsseldorf, D-40000

来源：

JOURNAL OF INHERITED METABOLIC DISEASE | 1993年 / 16卷 / 05期

关键词：

D O I：

10.1007/BF00714298

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

[No abstract available]

引用

页码：912 / 913

页数：2

共 4 条

[1] BRANCHED-CHAIN AMINO-ACID FREE PARENTERAL-NUTRITION IN THE TREATMENT OF ACUTE METABOLIC DECOMPENSATION IN PATIENTS WITH MAPLE SYRUP URINE DISEASE [J].

BERRY, GT ;

HEIDENREICH, R ;

KAPLAN, P ;

LEVINE, F ;

MAZUR, A ;

PALMIERI, MJ ;

YUDKOFF, M ;

SEGAL, S .

NEW ENGLAND JOURNAL OF MEDICINE, 1991, 324 (03) :175-179

[2] EFFECT OF INSULIN AND PLASMA AMINO-ACID-CONCENTRATIONS ON LEUCINE METABOLISM IN MAN - ROLE OF SUBSTRATE AVAILABILITY ON ESTIMATES OF WHOLE-BODY PROTEIN-SYNTHESIS [J].

CASTELLINO, P ;

LUZI, L ;

SIMONSON, DC ;

HAYMOND, M ;

DEFRONZO, RA .

JOURNAL OF CLINICAL INVESTIGATION, 1987, 80 (06) :1784-1793

[3] PHENYLALANINE LEVELS IN PKU FOLLOWING MINOR SURGERY [J].

FIEDLER, AE ;

MILLER, MJ ;

BICKEL, H ;

CEDERBAUM, SD .

AMERICAN JOURNAL OF MEDICAL GENETICS, 1982, 11 (04) :411-414

[4] DOSE-RESPONSE CURVES OF EFFECTS OF INSULIN ON LEUCINE KINETICS IN HUMANS [J].

TESSARI, P ;

TREVISAN, R ;

INCHIOSTRO, S ;

BIOLO, G ;

NOSADINI, R ;

DEKREUTZENBERG, SV ;

DUNER, E ;

TIENGO, A ;

CREPALDI, G .

AMERICAN JOURNAL OF PHYSIOLOGY, 1986, 251 (03) :E334-E342

← 1 →