CYSTINE - COMPARTMENTALIZATION WITHIN LYSOSOMES IN CYSTINOTIC LEUKOCYTES

被引：94

作者：

SCHULMAN, JD

BRADLEY, KH

SEEGMILL.JE

机构：

[1] Section on Human Biochemical Genetics, National Institute of Arthritis and Metabolic Diseases, Bethesda

来源：

SCIENCE | 1969年 / 166卷 / 3909期

关键词：

D O I：

10.1126/science.166.3909.1152

中图分类号：

O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];

学科分类号：

07 ; 0710 ; 09 ;

摘要：

The large amount of cystine compartmentalized in cystinotic leukocytes cosediments in isopycnic sucrose density gradients with dense lysosomal particles, within which it is presumably contained. Such cystine appears to be primarily noncrystalline in these organelles.

引用

页码：1152 / &

共 16 条

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