JUVENILE CHRONIC MYELOGENOUS LEUKEMIA AND DERMAL HISTIOCYTOSIS - IN VON RECKLINGHAUSENS DISEASE

被引:26
作者
BESTAK, M
MILLER, DR
MOURADIAN, JS
机构
[1] CORNELL UNIV,MED CTR,NEW YORK HOSP,DEPT PATHOL,NEW YORK,NY 10021
[2] MEM SLOAN KETTERING CANC CTR,DEPT PEDIAT,NEW YORK,NY 10021
来源
AMERICAN JOURNAL OF DISEASES OF CHILDREN | 1979年 / 133卷 / 08期
关键词
D O I
10.1001/archpedi.1979.02130080071014
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
A 4-year-old boy with multiple café-au-lait spots and a family history of neurofibromatosis had generalized edema, histiocytic rash characterized by benign histiocytic infiltration, hepatomegaly, and life-threatening infection. Six months later, progressive splenomegaly led to juvenile chronic myelocytic leukemia that eventually proved fatal. The case represents an important association of diseases. (Am J Dis Child 133:831-833, 1979. © 1979, American Medical Association. All rights reserved.
引用
收藏
页码:831 / 833
页数:3
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