CARDIAC TRANSPLANTATION IN BECKER MUSCULAR-DYSTROPHY

被引:44
作者
QUINLIVAN, RM
DUBOWITZ, V
机构
[1] GUYS HOSP, CTR NEWCOMEN, MARJORIE CROWE NEUROMUSCULAR CLIN, LONDON SE1, ENGLAND
[2] ROYAL POSTGRAD MED SCH, DEPT PAEDIATR & NEONATAL MED, NEUROMUSCULAR CLIN, LONDON W12 0NN, ENGLAND
关键词
MUSCULAR DYSTROPHY; BECKER MUSCULAR DYSTROPHY; CARDIOMYOPATHY; CARDIAC FAILURE; CARDIAC TRANSPLANT;
D O I
10.1016/0960-8966(92)90002-N
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Becker muscular dystrophy is associated with abnormal cardiac features in about 75% of cases; up to one-third will develop ventricular dilatation leading to congestive cardiac failure. As this form of muscular dystrophy is relatively benign, failure to respond to medical treatment warrants assessment for cardiac transplantation.
引用
收藏
页码:165 / 167
页数:3
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