INTRAVASCULAR LYMPHOMATOSIS (NEOPLASTIC ANGIOENDOTHELIOSIS) OF THE CENTRAL-NERVOUS-SYSTEM - CASE-REPORT AND LITERATURE-REVIEW

被引:30
作者
SMADJA, D
MAS, JL
FALLETBIANCO, C
MEYNIARD, O
SICARD, D
DERECONDO, J
RONDOT, P
机构
[1] CTR HOSP ST ANNE,CTR RAYMOND GARCIN,SERV NEUROL,1 RUE CABANIS,F-75674 PARIS 14,FRANCE
[2] GRP HOSP COCHIN PORT ROYAL,DEPT MED INTERNE,F-75674 PARIS 14,FRANCE
[3] CTR HOSP ST ANNE,CTR RAYMOND GARCIN,SERV ANAT PATHOL,F-75674 PARIS 14,FRANCE
关键词
INTRAVASCULAR LYMPHOMATOSIS; CENTRAL NERVOUS SYSTEM; VASCULAR DEMENTIA; LACTICO DEHYDROGENASES;
D O I
10.1007/BF02390177
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
A 63-year-old woman developed gradual slowness, recurrent multifocal deficits, severe constitutional symptoms and hypopituitarism which progressed to death over 2.5 months. Elevation in lactico dehydrogenases was the main biological abnormality. Necropsy showed an intravascular malignant proliferation which proved to be a lymphoma of B-lineage. In order to better define diagnostic criteria, we reviewed previously reported cases of intravascular lymphomatosis of the central nervous system. A strategy for establishing the diagnosis is proposed.
引用
收藏
页码:171 / 180
页数:10
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