BLOOD-CLOTTING FACTOR-IX KASHIHARA - AMINO-ACID SUBSTITUTION OF VALINE-182 BY PHENYLALANINE

被引:20
作者
SAKAI, T
YOSHIOKA, A
YAMAMOTO, K
NIINOMI, K
FUJIMURA, Y
FUKUI, H
MIYATA, T
IWANAGA, S
机构
[1] NARA MED COLL,DEPT PEDIAT,KASHIHARA,NARA 634,JAPAN
[2] KYUSHU UNIV 33,FAC SCI,DEPT BIOL,HIGASHI KU,FUKUOKA 812,JAPAN
关键词
D O I
10.1093/oxfordjournals.jbchem.a122740
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:756 / 759
页数:4
相关论文
共 31 条
[1]   THE GENE STRUCTURE OF HUMAN ANTI-HEMOPHILIC FACTOR-IX [J].
ANSON, DS ;
CHOO, KH ;
REES, DJG ;
GIANNELLI, F ;
GOULD, K ;
HUDDLESTON, JA ;
BROWNLEE, GG .
EMBO JOURNAL, 1984, 3 (05) :1053-1060
[2]   DEFECTIVE PROPEPTIDE PROCESSING OF BLOOD-CLOTTING FACTOR-IX CAUSED BY MUTATION OF ARGININE TO GLUTAMINE AT POSITION -4 [J].
BENTLEY, AK ;
REES, DJG ;
RIZZA, C ;
BROWNLEE, GG .
CELL, 1986, 45 (03) :343-348
[3]  
BERTINA RM, 1982, THROMB HAEMOSTASIS, V47, P136
[4]   RAPID ANALYSIS OF AMINO-ACIDS USING PRE-COLUMN DERIVATIZATION [J].
BIDLINGMEYER, BA ;
COHEN, SA ;
TARVIN, TL .
JOURNAL OF CHROMATOGRAPHY, 1984, 336 (01) :93-104
[5]  
Bloom A. L., 1981, HAEMOSTASIS THROMBOS, P321
[6]   MOLECULAR-CLONING OF THE GENE FOR HUMAN ANTI-HEMOPHILIC FACTOR-IX [J].
CHOO, KH ;
GOULD, KG ;
REES, DJG ;
BROWNLEE, GG .
NATURE, 1982, 299 (5879) :178-180
[7]  
DAVIS LM, 1987, BLOOD, V69, P140
[8]   ACTIVATION OF HUMAN FACTOR-9 (CHRISTMAS-FACTOR) [J].
DISCIPIO, RG ;
KURACHI, K ;
DAVIE, EW .
JOURNAL OF CLINICAL INVESTIGATION, 1978, 61 (06) :1528-1538
[9]   MOLECULAR-BASIS OF HEMOPHILIA-B - A DEFECTIVE ENZYME DUE TO AN UNPROCESSED PROPEPTIDE IS CAUSED BY A POINT MUTATION IN THE FACTOR-IX PRECURSOR [J].
DIUGUID, DL ;
RABIET, MJ ;
FURIE, BC ;
LIEBMAN, HA ;
FURIE, B .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1986, 83 (16) :5803-5807
[10]   CHYMOTRYPSINOGEN - 2.5-A CRYSTAL STRUCTURE, COMPARISON WITH ALPHA-CHYMOTRYPSIN, AND IMPLICATIONS FOR ZYMOGEN ACTIVATION [J].
FREER, ST ;
KRAUT, J ;
ROBERTUS, JD ;
WRIGHT, HT ;
XUONG, NH .
BIOCHEMISTRY, 1970, 9 (09) :1997-&