INTESTINAL LYMPHANGIECTASIA WITH PROTEIN LOSING ENTEROPATHY, TOXIC COPPER ACCUMULATION AND HYPOPARATHYROIDISM

被引：7

作者：

ODONNELL, D ^{[1
]}

MYERS, AM ^{[1
]}

机构：

[1] JOHANNESBURG HOSP,DIV NEPHROL,JOHANNESBURG,SOUTH AFRICA

来源：

AUSTRALIAN AND NEW ZEALAND JOURNAL OF MEDICINE | 1990年 / 20卷 / 02期

关键词：

copper toxicity; hypoparathyroidism; Intestinal lymphangiectasia;

D O I：

10.1111/j.1445-5994.1990.tb01295.x

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Abstract A 13‐year‐old girl presented with malabsorption which was ascribed to intestinal lymphangiectasia. Three years later a generalised seizure resulted from hypocalcaemia that was shown to be due to hypoparathyroidism during investigation of which toxic copper accumulation was recognised. The chance occurrence of three rare conditions is extremely remote making intestinal lymphangiectasia likely as the primary pathology. It is suggested that chronic intestinal loss of the copper‐carrying caeruloplasmin resulted in toxic parathyroid deposition of copper leading to hypoparathyroidism with consequent hypocalcaemic seizure. Copyright © 1990, Wiley Blackwell. All rights reserved

引用

页码：167 / 169

页数：3

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