SPONTANEOUS INTRACRANIAL HYPOTENSION FROM A CSF LEAK IN A PATIENT WITH MARFANS-SYNDROME

被引:81
作者
DAVENPORT, RJ
CHATAWAY, SJS
WARLOW, CP
机构
[1] University of Edinburgh, Department of Clinical Neurosciences, Western General Hospital, Edinburgh EH4 2XU, Crewe Road
关键词
INTRACRANIAL HYPOTENSION; MARFANS SYNDROME; CISTEMOGRAPHY;
D O I
10.1136/jnnp.59.5.516
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A patient with Marfan's syndrome had spontaneous intracranial hypotension secondary to a proved CSF leak. It is postulated that the leak was caused by minor, unrecognised trauma rupturing spinal arachnoid diverticula. The diverticula were probably pre-existing abnormalities complicating the Marfan's syndrome. It is concluded that patients with spinal meningeal defects may be at increased risk of developing CSF leaks, possibly secondary to unrecognised trauma.
引用
收藏
页码:516 / 519
页数:4
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