THE INTRACELLULAR-TRANSPORT OF LOW-DENSITY LIPOPROTEIN DERIVED CHOLESTEROL IS DEFECTIVE IN NIEMANN-PICK TYPE-C FIBROBLASTS

被引：264

作者：

LISCUM, L

RUGGIERO, RM

FAUST, JR

机构：

来源：

JOURNAL OF CELL BIOLOGY | 1989年 / 108卷 / 05期

关键词：

D O I：

10.1083/jcb.108.5.1625

中图分类号：

Q2 [细胞生物学];

学科分类号：

071009 ; 090102 ;

摘要：

引用

页码：1625 / 1636

页数：12

共 36 条

[1]

Ames B.N, 1966, METHOD ENZYMOL, V8, P115, DOI DOI 10.1016/0076-6879(66)08014-5

[2] RAPID TRANSMEMBRANE MOVEMENT OF CHOLESTEROL IN SMALL UNILAMELLAR VESICLES [J].

BACKER, JM ;

DAWIDOWICZ, EA .

BIOCHIMICA ET BIOPHYSICA ACTA, 1979, 551 (02) :260-270

[3]

Barrett AJ, 1972, LYSOSOMES LABORATORY, P46

[4] TYPE-C NIEMANN-PICK DISEASE - LOW-DENSITY LIPOPROTEIN UPTAKE IS ASSOCIATED WITH PREMATURE CHOLESTEROL ACCUMULATION IN THE GOLGI-COMPLEX AND EXCESSIVE CHOLESTEROL STORAGE IN LYSOSOMES [J].

BLANCHETTEMACKIE, EJ ;

DWYER, NK ;

AMENDE, LM ;

KRUTH, HS ;

BUTLER, JD ;

SOKOL, J ;

COMLY, ME ;

VANIER, MT ;

AUGUST, JT ;

BRADY, RO ;

PENTCHEV, PG .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1988, 85 (21) :8022-8026

[5]

BLIGH EG, 1959, CAN J BIOCHEM PHYS, V37, P911

[6]

Brady R. O., 1983, METABOLIC BASIS INHE, P831

[7] A RECEPTOR-MEDIATED PATHWAY FOR CHOLESTEROL HOMEOSTASIS [J].

BROWN, MS ;

GOLDSTEIN, JL .

SCIENCE, 1986, 232 (4746) :34-47

[8]

BROWN MS, 1980, J LIPID RES, V21, P505

[9] ENZYMIC CHARACTERIZATION AND LIPID COMPOSITION OF RAT LIVER SUBCELLULAR MEMBRANES [J].

COLBEAU, A ;

NACHBAUR, J ;

VIGNAIS, PM .

BIOCHIMICA ET BIOPHYSICA ACTA, 1971, 249 (02) :462-+

[10] DYNAMICS OF MEMBRANE LIPID-METABOLISM AND TURNOVER [J].

DAWIDOWICZ, EA .

ANNUAL REVIEW OF BIOCHEMISTRY, 1987, 56 :43-61

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