THE ROLE OF THE BLOOD-BRAIN BARRIER IN THE ETIOLOGY OF PERMANENT BRAIN-DYSFUNCTION IN HYPERPHENYLALANINEMIA

被引:17
作者
HOMMES, FA
机构
关键词
D O I
10.1007/BF01805529
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:41 / 46
页数:6
相关论文
共 32 条
[1]  
BANOS G, 1977, PSYCHOL MED, V4, P262
[2]  
BERGER R, 1980, CELL MOL BIOL, V26, P31
[3]   REDUCTION OF CEREBROSPINAL-FLUID PHENYLALANINE AFTER ORAL-ADMINISTRATION OF VALINE, ISOLEUCINE, AND LEUCINE [J].
BERRY, HK ;
BOFINGER, MK ;
HUNT, MM ;
PHILLIPS, PJ ;
GUILFOILE, MB .
PEDIATRIC RESEARCH, 1982, 16 (09) :751-755
[4]  
BERRY HK, 1985, DEV MED CHILD NEUROL, V27, P33
[5]  
Buist NRM, 1985, INHERITED DISEASES A, P203
[6]   WHERE DO THE DEPLETED PLASMA AMINO-ACIDS GO IN PHENYLKETONURIA [J].
CHRISTENSEN, HN .
BIOCHEMICAL JOURNAL, 1986, 236 (03) :929-930
[7]   HISTIDINEMIA .3. IMPACT - A PROSPECTIVE-STUDY [J].
COULOMBE, JT ;
KAMMERER, BL ;
LEVY, HL ;
HIRSCH, BZ ;
SCRIVER, CR .
JOURNAL OF INHERITED METABOLIC DISEASE, 1983, 6 (02) :58-61
[8]  
CURTIUS MC, 1981, ADV EXP MED BIOL, V133, P277
[9]  
ELSAS LJH, 1988, IETARY PHENYLALANINE, P187
[10]   TURNOVER OF THE FAST COMPONENTS OF MYELIN AND MYELIN PROTEINS IN EXPERIMENTAL HYPERPHENYLALANINEMIA - RELEVANCE TO TERMINATION OF DIETARY-TREATMENT IN HUMAN PHENYLKETONURIA [J].
HOMMES, FA ;
ELLER, AG ;
TAYLOR, EH .
JOURNAL OF INHERITED METABOLIC DISEASE, 1982, 5 (01) :21-27