CROWNED DENS SYNDROME - A MANIFESTATION OF HYDROXYAPATITE RHEUMATISM

被引:35
作者
MALCA, SA
ROCHE, PH
PELLET, W
COMBALBERT, A
机构
[1] Department of Neurosurgery, Hôpital Sainte Marguerite, Marseille
关键词
CROWNED ODONTOID; HYDROXYAPATITE RHEUMATISM; OCCIPITOCERVICAL REGION; ODONTOID PROCESS;
D O I
10.1007/BF02187755
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Crowned dens syndrome is defined as an association of acute cervical pain and calcifications in the peri-odontoid space. The authors report one case of this rare localization of hydroxy-apatite rheumatism and review 12 similar cases in the literature. This disease affects only adult females. Patients present with inflammatory signs, can be treated with non-steroid anti-inflammatory drugs and recover without sequela. Calcium pyrophosphate dihydrate deposition can also lead to this syndrome. Other perioodontoid calcifications and ossifications, usually asymptomatic, appear only as a radiologically crowned dens.
引用
收藏
页码:126 / 130
页数:5
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