THE DROPPED HEAD SYNDROME

被引:119
作者
SUAREZ, GA [1 ]
KELLY, JJ [1 ]
机构
[1] TUFTS UNIV,NEW ENGLAND MED CTR,DEPT NEUROL,BOSTON,MA 02111
关键词
D O I
10.1212/WNL.42.8.1625
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We describe four patients with a neuromuscular syndrome characterized by relatively isolated neck extensor weakness. EMG and muscle biopsies suggest a restrictive noninflammatory myopathy predominantly affecting the cervical paraspinal muscles.
引用
收藏
页码:1625 / 1627
页数:3
相关论文
共 10 条
[1]   CHRONIC FOCAL POLYMYOSITIS IN THE ADULT [J].
BHARUCHA, NE ;
MORGANHUGHES, JA .
JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1981, 44 (05) :419-425
[2]  
Bohan A, 1988, POLYMYOSITIS DERMATO, P19
[3]   POLYMYOSITIS - ITS PRESENTATION, MORBIDITY AND MORTALITY [J].
DEVERE, R ;
BRADLEY, WG .
BRAIN, 1975, 98 (DEC) :637-666
[4]   POLYMYOSITIS BEGINNING AS A FOCAL PROCESS [J].
HEFFNER, RR ;
BARRON, SA .
ARCHIVES OF NEUROLOGY, 1981, 38 (07) :439-442
[5]   SYNDROME OF SYSTEMIC CARNITINE DEFICIENCY - CLINICAL, MORPHOLOGIC, BIOCHEMICAL, AND PATHOPHYSIOLOGIC FEATURES [J].
KARPATI, G ;
CARPENTER, S ;
ENGEL, AG ;
WATTERS, G ;
ALLEN, J ;
ROTHMAN, S ;
KLASSEN, G ;
MAMER, OA .
NEUROLOGY, 1975, 25 (01) :16-24
[6]  
LANGE DJ, 1986, ANN NEUROL, V20, P133
[7]  
Munsat T, 1974, Bull Los Angeles Neurol Soc, V39, P113
[8]  
Ringel SP, 1979, HDB CLIN NEUROLOGY, P295
[9]   HEREDITARY CARNITINE DEFICIENCY OF MUSCLE [J].
VANDYKE, DH ;
GRIGGS, RC ;
MARKESBERY, W ;
DIMAURO, S .
NEUROLOGY, 1975, 25 (02) :154-159
[10]   POLYMYOSITIS PRESENTING WITH CHRONIC PROGRESSIVE DISTAL MUSCULAR WEAKNESS [J].
VANKASTEREN, BJ .
JOURNAL OF THE NEUROLOGICAL SCIENCES, 1979, 41 (03) :307-310