AMYLOID MYOPATHY PRESENTING WITH RESPIRATORY-FAILURE

被引：19

作者：

ASHE, J

BOREL, CO

HART, G

HUMPHREY, RL

DERRICK, DA

KUNCL, RW

机构：

[1] JOHNS HOPKINS UNIV HOSP,DEPT ANESTHESIOL & CLIN CARE MED,BALTIMORE,MD 21205

[2] JOHNS HOPKINS UNIV HOSP,DEPT ONCOL,BALTIMORE,MD 21205

[3] JOHNS HOPKINS UNIV HOSP,DEPT PATHOL,BALTIMORE,MD 21205

来源：

JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY | 1992年 / 55卷 / 02期

关键词：

D O I：

10.1136/jnnp.55.2.162

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

Amyloidosis is a rare cause of myopathy. Its prominent or presenting feature may be respiratory failure. Physiological measurement of transdiaphragmatic pressure and biopsy specimens of muscle show the pathological mechanism to be diaphragm weakness due to amyloid infiltration of the diaphragm rather than parenchymal lung involvement. Thus amyloid myopathy even without the typical macroglossia and muscle pseudohypertrophy should be considered as one of the neurological causes of respiratory failure.

引用

页码：162 / 165

页数：4

共 18 条

[1] EFFECT OF PRESSURE AND TIMING OF CONTRACTION ON HUMAN DIAPHRAGM FATIGUE [J].