EFFECT OF COPPER ON MENKES AND NORMAL CULTURED SKIN FIBROBLASTS

被引:9
作者
BERATIS, NG [1 ]
YEE, M [1 ]
LABADIE, GU [1 ]
HIRSCHHORN, K [1 ]
机构
[1] CUNY MT SINAI SCH MED,DEPT PEDIAT,DIV MED GENET,NEW YORK,NY 10028
来源
DEVELOPMENTAL PHARMACOLOGY AND THERAPEUTICS | 1980年 / 1卷 / 05期
关键词
D O I
10.1159/000455548
中图分类号
R9 [药学];
学科分类号
1007 ;
摘要
引用
收藏
页码:305 / 317
页数:13
相关论文
共 17 条
[1]   CU-64 METABOLISM IN MENKES AND NORMAL CULTURED SKIN FIBROBLASTS [J].
BERATIS, NG ;
PRICE, P ;
LABADIE, G ;
HIRSCHHORN, K .
PEDIATRIC RESEARCH, 1978, 12 (06) :699-702
[2]   ARYLSULFATASE B DEFICIENCY IN MAROTEAUX-LAMY SYNDROME - CELLULAR STUDIES AND CARRIER IDENTIFICATION [J].
BERATIS, NG ;
TURNER, BM ;
WEISS, R ;
HIRSCHHORN, K .
PEDIATRIC RESEARCH, 1975, 9 (05) :475-480
[3]   CELL-CULTURE STUDIES OF MENKES KINKY HAIR DISEASE [J].
CHAN, WY ;
GARNICA, AD ;
RENNERT, OM .
CLINICA CHIMICA ACTA, 1978, 88 (03) :495-507
[4]   MENKESS SYNDROME - REPORT OF A PATIENT TREATED FROM 21 DAYS OF AGE WITH PARENTERAL COPPER [J].
DAISH, P ;
WHEELER, EM ;
ROBERTS, PF ;
JONES, RD .
ARCHIVES OF DISEASE IN CHILDHOOD, 1978, 53 (12) :956-958
[5]  
DANKS DM, 1973, LANCET, V1, P891
[6]  
DANKS DM, 1972, LANCET, V1, P1100
[7]  
DANKS DM, 1972, PEDIATRICS, V50, P188
[8]   MENKES KINKY HAIR DISEASE - FURTHER DEFINITION OF DEFECT IN COPPER TRANSPORT [J].
DANKS, DM ;
CARTWRIGHT, E ;
STEVENS, BJ ;
TOWNLEY, RRW .
SCIENCE, 1973, 179 (4078) :1140-1142
[9]  
DECABAN AS, 1975, ARCH NEUROL, V32, P672
[10]  
GARNICA AD, 1977, CLIN GENET, V11, P154, DOI 10.1111/j.1399-0004.1977.tb01294.x