MALIGNANT RHABDOID TUMOR - PRIMARY INTRACRANIAL MANIFESTATION IN AN ADULT

被引:78
作者
HORN, M
SCHLOTE, W
LERCH, KD
STEUDEL, WI
HARMS, D
THOMAS, E
机构
[1] STADT KLINIKEN DORTMUND, NEUROCHIRURG KLIN, W-4600 DORTMUND, GERMANY
[2] UNIV FRANKFURT, ZENTRUM NEUROL & NEUROCHIRURG, W-6000 FRANKFURT, GERMANY
[3] UNIV KIEL, INST PATHOL, PAIDOPATHOL ABT, W-2300 KIEL 1, GERMANY
关键词
MALIGNANT RHABDOID TUMOR; ADULTS; PRIMARY INTRACRANIAL MANIFESTATION;
D O I
10.1007/BF00713540
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Clinical, histopathological, and ultrastructural features of an extended intracranial malignant neoplasm are presented. Following incomplete extirpation of a large epidural tumor at the temporal base of the skull, the 21-year-old male patient suffered from several local recurrences and died at the age of 27. The neoplasm was defined by its histopathological and ultrastructural characteristics and by the pattern of its antigenicity as a malignant rhabdoid tumor (MRT). Considering previous publications on MRT, this case may be the first of primary intracranial MRT appearing in an adult.
引用
收藏
页码:445 / 448
页数:4
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