ISOLATION AND CHARACTERIZATION OF BETA-HYDROXYPROPIONIC ACID UROPORPHYRIN AND HYDROXYACETIC ACID UROPORPHYRIN-I IN THE URINE OF A PATIENT WITH CONGENITAL ERYTHROPOIETIC PORPHYRIA BY HIGH-PERFORMANCE LIQUID-CHROMATOGRAPHY AND LIQUID SECONDARY ION MASS-SPECTROMETRY

被引:9
作者
GUO, R
CHAI, W
RIDEOUT, JM
LAWSON, AM
LIM, CK
机构
[1] MRC,CTR CLIN RES,DIV CLIN CELL BIOL,WATFORD RD,HARROW HA1 3UJ,MIDDX,ENGLAND
[2] MRC,CTR CLIN RES,CLIN MASS SPECTROMETRY SECT,HARROW HA1 3UJ,MIDDX,ENGLAND
关键词
D O I
10.1002/bmc.1130040404
中图分类号
Q5 [生物化学];
学科分类号
071010 ; 081704 ;
摘要
β‐Hydroxypropionic acid‐ and hydroxyacetic acid‐uroporphyrin I have been isolated from the urine of a patient with congenital erythropoietic porphyria by reversed phase high performance liquid chromatography. The compounds were characterized by their chemical behaviour and confirmed by liquid secondary ion mass spectrometry. Copyright © 1990 John Wiley & Sons, Ltd.
引用
收藏
页码:141 / 143
页数:3
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