HEMODIALYSIS-RELATED PORPHYRIA-CUTANEA-TARDA AND TREATMENT BY RECOMBINANT-HUMAN-ERYTHROPOIETIN

被引:22
作者
YAQOOB, M
SMYTH, J
AHMAD, R
MCCLELLAND, P
FAHAL, I
KUMAR, KAS
YU, R
VERBOV, J
机构
[1] UNIV HOSP CARDIFF, DEPT BIOCHEM, CARDIFF, WALES
[2] ROYAL LIVERPOOL HOSP, REG RENAL UNIT, LIVERPOOL L7 8XP, MERSEYSIDE, ENGLAND
[3] ROYAL LIVERPOOL HOSP, DEPT DERMATOL, LIVERPOOL L7 8XP, MERSEYSIDE, ENGLAND
关键词
PORPHYRIA CUTANEA TARDA; HEMODIALYSIS; RECOMBINANT HUMAN ERYTHROPOIETIN;
D O I
10.1159/000186803
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
Haemodialysis-related porphyria cutanea tarda is a rare, but serious and mutilating skin condition, resulting from extremely high plasma porphyrin levels because of their inadequate clearance by haemodialysis. The treatment is very difficult as chloroquine is ineffective and venesection, the conventional treatment of this disease, is not always an option because of anaemia of end-stage renal disease. We report a case of haemodialysis-related porphyria cutanea tarda and her successful management by recombinant human erythropoietin treatment.
引用
收藏
页码:428 / 431
页数:4
相关论文
共 20 条
[1]   ERYTHROPOIETIN FOR THE TREATMENT OF PORPHYRIA CUTANEA-TARDA IN A PATIENT ON LONG-TERM HEMODIALYSIS [J].
ANDERSON, KE ;
GOEGER, DE ;
CARSON, RW ;
LEE, SMK ;
STEAD, RB .
NEW ENGLAND JOURNAL OF MEDICINE, 1990, 322 (05) :315-317
[2]   PORPHYRIAS AND THE KIDNEY [J].
DAY, RS ;
EALES, L ;
DISLER, PB .
NEPHRON, 1981, 28 (06) :261-267
[3]   PORPHYRINS IN CHRONIC-RENAL-FAILURE [J].
DAY, RS ;
EALES, L .
NEPHRON, 1980, 26 (02) :90-95
[4]  
de Verneuil H, 1978, Hum Genet, V44, P145
[5]   TREATMENT OF HEMODIALYSIS-RELATED PORPHYRIA CUTANEA-TARDA WITH PLASMA-EXCHANGE [J].
DISLER, P ;
DAY, R ;
BURMAN, N ;
BLEKKENHORST, G ;
EALES, L .
AMERICAN JOURNAL OF MEDICINE, 1982, 72 (06) :989-993
[6]  
ELDER GH, 1985, LANCET, V2, P229
[7]   CORRECTION OF THE ANEMIA OF END-STAGE RENAL-DISEASE WITH RECOMBINANT-HUMAN-ERYTHROPOIETIN - RESULTS OF A COMBINED PHASE-I AND PHASE-II CLINICAL-TRIAL [J].
ESCHBACH, JW ;
EGRIE, JC ;
DOWNING, MR ;
BROWNE, JK ;
ADAMSON, JW .
NEW ENGLAND JOURNAL OF MEDICINE, 1987, 316 (02) :73-78
[8]  
GOODILL JJ, 1987, NEW ENGL J MED, V317, P54
[9]  
HARLAN SL, 1983, MAYO CLIN PROC, V58, P467
[10]   BINDING OF C 14-LABELLED PORPHYRINS BY PLASMA PROTEINS [J].
KOSKELO, P ;
TOIVONEN, I ;
RINTOLA, P .
CLINICA CHIMICA ACTA, 1970, 29 (03) :559-&