2 CASES OF NEOPLASTIC ANGIOENDOTHELIOMATOSIS PRESENTING WITH MYELOPATHY

被引:24
作者
HAMADA, K
HAMADA, T
SATOH, M
TASHIRO, K
KATOH, I
NAGANUMA, M
SHIMA, K
OGATA, A
NAGASHIMA, K
机构
[1] HOKKAIDO UNIV,SCH MED,DEPT NEUROL,SAPPORO,HOKKAIDO 060,JAPAN
[2] HOKKAIDO UNIV,SCH MED,DEPT PATHOL,SAPPORO,HOKKAIDO 060,JAPAN
[3] NATL SAPPORO HOSP,SAPPORO,JAPAN
关键词
D O I
10.1212/WNL.41.7.1139
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We describe two patients with autopsy-proven neoplastic angioendotheliomatosis (NAE) presenting only as a transverse myelopathy for 10 to 12 months, followed by disseminated intracranial manifestations. Postmortem examination disclosed a vasculocentric distribution of neoplastic cells in various organs that stained positively with B-lymphocyte-specific monoclonal antibody. These cases were unusual because they manifested as an isolated myelopathy for many months.
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页码:1139 / 1140
页数:2
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