AGAROSE-GEL ISOELECTROFOCUSING OF UDP-GALACTOSE PYROPHOSPHORYLASE AND GALACTOSE-1-PHOSPHATE URIDYLTRANSFERASE - DEVELOPMENTAL ASPECT OF UDP-GALACTOSE PYROPHOSPHORYLASE

被引:26
作者
SHIN, YS
NIEDERMEIER, HP
ENDRES, W
SCHAUB, J
WEIDINGER, S
机构
[1] UNIV KIEL,CHILDRENS HOSP,D-2300 KIEL 1,FED REP GER
[2] INST ANTHROPOL & HUMAN GENET,MUNICH,FED REP GER
关键词
D O I
10.1016/0009-8981(87)90191-4
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
摘要
引用
收藏
页码:27 / 35
页数:9
相关论文
共 19 条
[1]   THE AMINO-ACIDURIA IN GALACTOSAEMIA [J].
CUSWORTH, DC ;
DENT, CE ;
FLYNN, FV .
ARCHIVES OF DISEASE IN CHILDHOOD, 1955, 30 (150) :150-154
[2]  
GITZELMANN R, 1965, PEDIATRICS, V36, P231
[3]  
GITZELMANN R, 1967, EXP EYE RES, V61, P1
[4]   CONGENITAL GALACTOSEMIA, A SINGLE ENZYMATIC BLOCK IN GALACTOSE METABOLISM [J].
ISSELBACHER, KJ ;
ANDERSON, EP ;
KURAHASHI, K ;
KALCKAR, HM .
SCIENCE, 1956, 123 (3198) :635-636
[5]  
ISSELBACHER KJ, 1957, J BIOL CHEM, V126, P651
[6]  
ISSELBACHER KJ, 1957, SCIENCE, V126, P651
[7]   URIDYL TRANSFERASES AND THE FORMATION OF URIDINE DIPHOSPHOGALACTOSE [J].
KALCKAR, HM ;
BRAGANCA, B ;
MUNCHPETERSEN, A .
NATURE, 1953, 172 (4388) :1038-1038
[8]  
KNOP JK, 1970, J BIOL CHEM, V245, P2499
[9]  
LELOIR LF, 1951, PHOSPHORUS METABOL, V1, P67
[10]  
SCHWARZ V, 1953, BIOCH BIOPHYS ACTA, V18, P310