PREMATURE TERMINATION OF VARIABLE GENE REARRANGEMENT IN LYMPHOCYTES-B FROM X-LINKED AGAMMAGLOBULINEMIA

被引:21
作者
SCHWABER, J [1 ]
CHEN, RH [1 ]
机构
[1] HARVARD UNIV,SCH MED,DEPT PATHOL,BOSTON,MA 02115
关键词
D O I
10.1172/JCI113550
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:2004 / 2009
页数:6
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共 38 条
[1]   JOINING OF IMMUNOGLOBULIN HEAVY-CHAIN GENE SEGMENTS - IMPLICATIONS FROM A CHROMOSOME WITH EVIDENCE OF 3 D-JH FUSIONS [J].
ALT, FW ;
BALTIMORE, D .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (13) :4118-4122
[3]   ISOLATION OF BIOLOGICALLY-ACTIVE RIBONUCLEIC-ACID FROM SOURCES ENRICHED IN RIBONUCLEASE [J].
CHIRGWIN, JM ;
PRZYBYLA, AE ;
MACDONALD, RJ ;
RUTTER, WJ .
BIOCHEMISTRY, 1979, 18 (24) :5294-5299
[4]  
COOPER M, 1985, PRIMARY IMMUNODEFICI, P63
[5]   CHROMOSOMAL LOCATION OF THE GENES FOR HUMAN-IMMUNOGLOBULIN HEAVY-CHAINS [J].
CROCE, CM ;
SHANDER, M ;
MARTINIS, J ;
CICUREL, L ;
DANCONA, GG ;
DOLBY, TW ;
KOPROWSKI, H .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1979, 76 (07) :3416-3419
[6]   PHYSICAL CHANGE IN CYTOPLASMIC MESSENGER RIBONUCLEOPROTEINS IN CELLS TREATED WITH INHIBITORS OF MESSENGER-RNA TRANSCRIPTION [J].
DREYFUSS, G ;
ADAM, SA ;
CHOI, YD .
MOLECULAR AND CELLULAR BIOLOGY, 1984, 4 (03) :415-423
[7]   AN IMMUNOGLOBULIN HEAVY-CHAIN VARIABLE REGION GENE IS GENERATED FROM 3 SEGMENTS OF DNA - VH, D AND JH [J].
EARLY, P ;
HUANG, H ;
DAVIS, M ;
CALAME, K ;
HOOD, L .
CELL, 1980, 19 (04) :981-992
[8]   IDENTIFICATION AND CHARACTERIZATION OF SUBPOPULATION OF LYMPHOCYTES IN HUMAN PERIPHERAL-BLOOD AFTER FRACTIONATION ON DISCONTINUOUS GRADIENTS OF ALBUMIN - CELLULAR DEFECT IN X-LINKED AGAMMAGLOBULINEMIA [J].
GEHA, RS ;
ROSEN, FS ;
MERLER, E .
JOURNAL OF CLINICAL INVESTIGATION, 1973, 52 (07) :1726-1734
[9]   ISOLATION AND PARTIAL CHARACTERIZATION OF THE DROSOPHILA ALCOHOL-DEHYDROGENASE GENE [J].
GOLDBERG, DA .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1980, 77 (10) :5794-5798
[10]   A SIMPLE AND VERY EFFICIENT METHOD FOR GENERATING CDNA LIBRARIES [J].
GUBLER, U ;
HOFFMAN, BJ .
GENE, 1983, 25 (2-3) :263-269