INFLAMMATORY MYOPATHY IN OCULOPHARYNGEAL DYSTROPHY

被引:19
作者
BOSCH, EP
GOWANS, JDC
MUNSAT, T
机构
[1] TUFTS UNIV,NEW ENGLAND MED CTR,DEPT NEUROL,BOSTON,MA 02111
[2] TUFTS UNIV,NEW ENGLAND MED CTR,NEUROMUSCULAR UNIT,BOSTON,MA 02111
[3] TUFTS UNIV,NEW ENGLAND MED CTR,DEPT INTERNAL MED,BOSTON,MA 02111
关键词
D O I
10.1002/mus.880020111
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A 75‐year‐old French‐Canadian woman with familial oculopharyngeal dystrophy demonstrated histopathologic alterations similar to those of idiopathic polymyositis. A second biopsy obtained 15 months later was more consistent with previously reported cases. It is suggested that certain patients with oculopharyngeal dystrophy may pass through an initial phase of secondary muscle inflammation similar to that seen in some other heritable myopathies. Copyright © 1979 Houghton Mifflin Professional Publishers
引用
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页码:73 / 77
页数:5
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