PEROXISOMAL L-PIPECOLIC ACID OXIDATION IS DEFICIENT IN LIVER FROM ZELLWEGER SYNDROME PATIENTS

被引：37

作者：

MIHALIK, SJ

MOSER, HW

WATKINS, PA

DANKS, DM

POULOS, A

RHEAD, WJ

机构：

[1] UNIV IOWA HOSP & CLIN, DEPT PEDIAT, IOWA CITY, IA 52242 USA

[2] KENNEDY INST HANDICAPPED CHILDREN, BALTIMORE, MD 21205 USA

[3] ROYAL CHILDRENS HOSP, MURDOCH INST, PARKVILLE, VIC 3052, AUSTRALIA

[4] ADELAIDE CHILDRENS HOSP, DEPT CHEM PATHOL, Adelaide, SA 5006, AUSTRALIA

来源：

PEDIATRIC RESEARCH | 1989年 / 25卷 / 05期

关键词：

D O I：

10.1203/00006450-198905000-00024

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

引用

页码：548 / 552

页数：5

共 36 条

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