KERATOSIS PILARIS ATROPHICANS FACIEI (ULERYTHEMA OPHRYOGENES) - CUTANEOUS MARKER IN THE NOONAN SYNDROME

被引:53
作者
PIERINI, DO
PIERINI, AM
机构
[1] PEDRO ELIZALDE GEN HOSP CHILDREN,DEPT DERMATOL,BUENOS AIRES,ARGENTINA
[2] BUENOS AIRES NATL UNIV,BUENOS AIRES,ARGENTINA
关键词
D O I
10.1111/j.1365-2133.1979.tb01641.x
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Five cases are reported of Noonan's syndrome, all of which presented keratosis pilaris atrophicans faciei (ulerythema ophryogenes). This dermatosis fulfils the criteria mentioned by Noonan & Ehmke (1963) as a pointer for the investigation of cardiac anomalies, especially of the pulmonary artery. Copyright © 1979, Wiley Blackwell. All rights reserved
引用
收藏
页码:409 / 416
页数:8
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