PRENATAL-DIAGNOSIS OF A MULTIFOCAL LYMPHANGIOMA

被引:7
作者
GIACALONE, PL
BOULOT, P
DESCHAMPS, F
NAGY, P
HEDON, B
LAFFARGUE, F
VIALA, JL
机构
[1] Fetology Center, Department of Obstetrics and Gynecology, Hôpital Arnaud de Villeneuve, Montpellier, 34059, Route de Ganges
关键词
PRENATAL DIAGNOSIS; CERVICAL LYMPHANGIOMA; MEDIASTINAL LYMPHANGIOMA; ABDOMINAL LYMPHANGIOMA;
D O I
10.1002/pd.1970131208
中图分类号
Q3 [遗传学];
学科分类号
071007 [遗传学]; 090102 [作物遗传育种];
摘要
Lymphangiomas or cystic hygromas are malformations of the lymphatic vessels and are characterized by single or multiple cysts which have developed within the soft tissues. They occur most commonly in the neck (75 per cent of cases) and are often associated with hydrops or chromosomal abnormalities (Romero et al., 1988). Mediastinal or abdominal locations are rare and represent less than 5 per cent of cases in the literature (Singh et al., 1971). This paper represents the first reported case of prenatal diagnosis of a lymphangioma in the neck, mediastinum, and abdomen. Diagnosis was made before fetal viability, and allowed us to recommend termination of the pregnancy because of the poor prognosis.
引用
收藏
页码:1133 / 1137
页数:5
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