ULTRASONOGRAPHY, CT, AND MRI OF MUSCLES IN CONGENITAL NEMALINE MYOPATHY

被引：33

作者：

WALLGRENPETTERSSON, C

KIVISAARI, L

JAASKELAINEN, J

LAMMINEN, A

HOLMBERG, C

机构：

[1] Children's Hospital, University of Helsinki, Helsinki

[2] Department of Diagnostic Radiology, University of Helsinki, Helsinki

来源：

PEDIATRIC NEUROLOGY | 1990年 / 6卷 / 01期

关键词：

D O I：

10.1016/0887-8994(90)90074-B

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

Twelve patients with congenital nemaline myopathy were examined by ultrasonography and computed tomography (CT) and 4 of them by low-field magnetic resonance imaging (MRI) to investigate the distribution and nature of muscle involvement and to evaluate the yield of these techniques. A pattern of selective muscle involvement was consistently found. Ultrasonography revealed abnormally high muscle echogenicity. In contrast to the controls with simple disuse and/or neurogenic atrophy, CT revealed low muscle density in our patients. MRI confirmed that this pattern reflects patchy, fatty degeneration, a new finding in congenital nemaline myopathy. Ultrasonography appears useful for screening, provided that the dorsiflexors of the feet are examined. CT and MRI can be used to demonstrate abnormalities in mild cases, to select the biopsy site, and for follow-up. MRI, because it provides good soft tissue contrast, is useful for determining fatty infiltration. © 1990.

引用

页码：20 / 28

页数：9

共 36 条

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