EFFECTS OF CYSTEAMINE THERAPY IN NEPHROPATHIC CYSTINOSIS

被引:64
作者
YUDKOFF, M
FOREMAN, JW
SEGAL, S
机构
[1] UNIV PENN,SCH MED,DEPT PEDIAT,PHILADELPHIA,PA 19104
[2] UNIV PENN,SCH MED,DEPT MED,PHILADELPHIA,PA 19104
关键词
D O I
10.1056/NEJM198101153040303
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:141 / 145
页数:5
相关论文
共 35 条
[1]  
ARANT BS, 1976, PEDIATRICS, V58, P370
[2]  
BAAR HS, 1952, ACTA PAEDIATR SCAN S, V90, P171
[3]  
BACQ ZM, 1965, CHEM PROTECTION IONI, P16
[4]  
BAUER B, 1966, HELV PAEDIATR ACTA, V21, P19
[5]  
BICKEL H, 1955, Helv Paediatr Acta, V10, P259
[6]   HYPOTHYROIDISM IN CYSTINOSIS - A CLINICAL, ENDOCRINOLOGIC AND HISTOLOGIC STUDY INVOLVING 16 PATIENTS WITH CYSTINOSIS [J].
CHAN, AM ;
LYNCH, MJG ;
BAILEY, JD ;
EZRIN, C ;
FRASER, D .
AMERICAN JOURNAL OF MEDICINE, 1970, 48 (06) :678-&
[7]  
CLAYTON BE, 1961, LANCET, V2, P909
[8]   CYSTINOSIS - PLASMA CYSTINE AND CYSTEINE CONCENTRATIONS AND EFFECT OF D-PENICILLAMINE AND DIETARY TREATMENT [J].
CRAWHALL, JC ;
LIETMAN, PS ;
SCHNEIDER, JA ;
SEEGMILLER, JE .
AMERICAN JOURNAL OF MEDICINE, 1968, 44 (03) :330-+
[9]   INVIVO USE OF DITHIOTHREITOL IN CYSTINOSIS [J].
DEPAPEBRIGGER, D ;
GOLDMAN, H ;
SCRIVER, CR ;
DELVIN, E ;
MAMER, O .
PEDIATRIC RESEARCH, 1977, 11 (02) :124-131
[10]   TREATMENT OF CYSTINOSIS WITH CYSTEAMINE [J].
GIRARDIN, EP ;
DEWOLFE, MS ;
CROCKER, JFS .
JOURNAL OF PEDIATRICS, 1979, 94 (05) :838-840