BREAKDOWN OF LYSOSOMAL GLYCOGEN IN CULTURED FIBROBLASTS FROM GLYCOGENOSIS TYPE-II PATIENTS AFTER UPTAKE OF ACID ALPHA-GLUCOSIDASE

被引：28

作者：

VANDERPLOEG, AT

KROOS, M

VANDONGEN, JM

VISSER, WJ

BOLHUIS, PA

LOONEN, MCB

REUSER, AJJ

机构：

[1] ERASMUS UNIV,DEPT NEUROL,3000 DR ROTTERDAM,NETHERLANDS

[2] UNIV AMSTERDAM,ACAD MED CTR,DEPT NEUROL,1105 AZ AMSTERDAM,NETHERLANDS

来源：

JOURNAL OF THE NEUROLOGICAL SCIENCES | 1987年 / 79卷 / 03期

关键词：

D O I：

10.1016/0022-510X(87)90239-5

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

引用

页码：327 / 336

页数：10

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