INTERCURRENT ILLNESS IN INBORN-ERRORS OF INTERMEDIARY METABOLISM

被引：62

作者：

DIXON, MA

LEONARD, JV

机构：

[1] INST CHILD HLTH,MED UNIT,30 GUILFORD ST,LONDON WC1N 1EH,ENGLAND

[2] HOSP SICK CHILDREN,LONDON WC1N 3JH,ENGLAND

来源：

ARCHIVES OF DISEASE IN CHILDHOOD | 1992年 / 67卷 / 11期

关键词：

D O I：

10.1136/adc.67.11.1387

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Metabolic decompensation may occur in patients with disorders of intermediary metabolism during intercurrent illness. To prevent complications it is normal practice to change the diet to an 'emergency regimen'. The mainstay of this is a high carbohydrate intake, using soluble glucose polymer, given as frequent drinks by day and during the night. Additional therapy is given for some disorders. Practical details of the treatment are outlined.

引用

页码：1387 / 1391

页数：5

共 7 条

[1] RENAL TUBULAR DYSFUNCTION IN METHYLMALONIC ACIDEMIA [J].

DANGIO, CT ;

DILLON, MJ ;

LEONARD, JV .

EUROPEAN JOURNAL OF PEDIATRICS, 1991, 150 (04) :259-263

[2]

Newsholme E.A., 1983, BIOCH MED SCI

[3] MUSCLE PROTEIN-SYNTHESIS MEASURED BY STABLE ISOTOPE TECHNIQUES IN MAN - THE EFFECTS OF FEEDING AND FASTING [J].

RENNIE, MJ ;

EDWARDS, RHT ;

HALLIDAY, D ;

MATTHEWS, DE ;

WOLMAN, SL ;

MILLWARD, DJ .

CLINICAL SCIENCE, 1982, 63 (06) :519-523

[4]

SBAI D, 1992, Pediatric Research, V31, p188A

[5]

Scriver CR, 1989, METABOLIC BASIS INHE

[6]

THOMPSON GN, 1991, METABOLISM, V119, P35

[7]

THOMPSON GN, 1990, AM J PHYSIOL, V254, P654

← 1 →