A FAMILIAL FORM OF INCOMPLETE SEPTAL CIRRHOSIS

被引:22
作者
BARNETT, JL
APPELMAN, HD
MOSELEY, RH
机构
[1] UNIV MICHIGAN,SCH MED,DEPT INTERNAL MED,DIV GASTROENTEROL,ANN ARBOR,MI 48104
[2] UNIV MICHIGAN,SCH MED,DEPT PATHOL,ANN ARBOR,MI 48104
[3] VET AFFAIRS MED CTR,ANN ARBOR,MI
关键词
D O I
10.1016/0016-5085(92)90119-J
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
The clinical features and hepatic histology of a disorder resembling idiopathic portal hypertension and nodular regenerative hyperplasia but most consistent with incomplete septal cirrhosis, occurring in four family members, are described. This represents the first description of the familial occurrence of this entity. Features common to incomplete septal cirrhosis and the noncirrhotic nodular conditions of the liver that may present with complications of portal hypertension are discussed. © 1992.
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收藏
页码:674 / 678
页数:5
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